{"id":12738,"date":"2025-07-22T08:25:54","date_gmt":"2025-07-22T12:25:54","guid":{"rendered":"https:\/\/www.rigicon.com\/glossary-term\/angiomyolipoma\/"},"modified":"2025-07-22T08:25:54","modified_gmt":"2025-07-22T12:25:54","slug":"angiomiolipoma-pt-br","status":"publish","type":"glossary-term","link":"https:\/\/www.rigicon.com\/pt-br\/glossary-term\/angiomiolipoma-pt-br\/","title":{"rendered":"Angiomiolipoma"},"content":{"rendered":"","protected":false},"excerpt":{"rendered":"","protected":false},"featured_media":0,"template":"","glossary-category":[126],"glossary-product":[],"class_list":["post-12738","glossary-term","type-glossary-term","status-publish","hentry","glossary-category-urological-conditions"],"acf":{"gt-definition":"<p>O angiomiolipoma \u00e9 um tumor renal benigno caracterizado por uma composi\u00e7\u00e3o de vasos sangu\u00edneos, m\u00fasculo liso e tecido adiposo em quantidades variadas.<span class=\"citation\">1<\/span> Pertence \u00e0 fam\u00edlia dos tumores de c\u00e9lulas epiteli\u00f3ides perivasculares (PEComas) e distingue-se pela sua diferencia\u00e7\u00e3o epiteli\u00f3ide perivascular.<span class=\"citation\">2<\/span> Estes tumores s\u00e3o tipicamente bem circunscritos e podem variar em tamanho de alguns mil\u00edmetros a mais de 20 cent\u00edmetros em di\u00e2metro.<span class=\"citation\">3<\/span> Embora considerados benignos, os angiomiolipomas podem crescer significativamente e causar complica\u00e7\u00f5es por efeito de massa ou hemorragia espont\u00e2nea devido \u00e0 presen\u00e7a de vasos sangu\u00edneos anormais com microaneurismas.<span class=\"citation\">4<\/span> Os angiomiolipomas podem se manifestar como massas ricas em gordura (mais comuns), pobres em gordura ou invis\u00edveis em gordura, com aproximadamente 5% pertencentes \u00e0 variedade pobre em gordura ou invis\u00edvel em gordura, que apresenta desafios diagn\u00f3sticos.<span class=\"citation\">5<\/span><\/p>\n<p>O angiomiolipoma \u00e9 um tumor renal benigno composto de tecido adiposo, muscular liso e vasos sangu\u00edneos an\u00f4malos. Representa 2-6% das neoplasias renais e pode ocorrer de forma espor\u00e1dica (80%) ou associado \u00e0 esclerose tuberosa (20%). O diagn\u00f3stico \u00e9 geralmente incidental em exames de imagem, identificado pela presen\u00e7a caracter\u00edstica de gordura macrosc\u00f3pica na tomografia computadorizada.<\/p>","gt-synonyms":"Angiomiolipoma renal (LMA), angiomiolipoma renal, LMA renal, LMA renal, hamartoma renal (embora tecnicamente distinto)","gt-citation":"[1] Skelton WP, Dahlen T, Patel H, et al. Renal Angiomyolipoma. StatPearls. 2024. https:\/\/www.ncbi.nlm.nih.gov\/books\/NBK585104\/\n\n[2] Jinzaki M, Silverman SG, Akita H, et al. Renal angiomyolipoma: a radiological classification and update on recent developments in diagnosis and management. Abdom Imaging. 2014;39(3):588-604. DOI: 10.1007\/s00261-014-0083-3\n\n[3] Flum AS, Hamoui N, Said MA, et al. Update on the Diagnosis and Management of Renal Angiomyolipoma. J Urol. 2016;195(4 Pt 1):834-846. DOI: 10.1016\/j.juro.2015.07.126\n\n[4] Bissler JJ, Kingswood JC. Renal angiomyolipomata. Kidney Int. 2018;93(6):1282-1294. DOI: 10.1016\/j.kint.2017.12.020\n\n[5] Vos N, Oyen R. Renal Angiomyolipoma: The Good, the Bad, and the Ugly. J Belg Soc Radiol. 2018;102(1):41. DOI: 10.5334\/jbsr.1536","gt-clinical-context":"<p>Os angiomiolipomas s\u00e3o clinicamente significativos em contextos espor\u00e1dicos e heredit\u00e1rios. A maioria (80%) ocorre esporadicamente, enquanto 20% est\u00e3o associados a condi\u00e7\u00f5es gen\u00e9ticas, principalmente complexo de esclerose tuberosa (CET) e linfangioleiomiomatose pulmonar (LAM).<span class=\"citation\">1<\/span><\/p>\n <p>Na pr\u00e1tica cl\u00ednica, os angiomiolipomas s\u00e3o frequentemente descobertos incidentalmente durante exames de imagem realizados por raz\u00f5es n\u00e3o relacionadas.<span class=\"citation\">2<\/span> No entanto, as apresenta\u00e7\u00f5es sintom\u00e1ticas podem incluir dor no flanco, massa palp\u00e1vel, infec\u00e7\u00f5es do trato urin\u00e1rio, hemat\u00faria, insufici\u00eancia renal ou hipertens\u00e3o.<span class=\"citation\">3<\/span> A apresenta\u00e7\u00e3o cl\u00ednica mais preocupante \u00e9 a hemorragia retroperitoneal espont\u00e2nea, que pode ser fatal e \u00e9 mais comum em tumores maiores que 4 cm em di\u00e2metro.<span class=\"citation\">4<\/span><\/p>\n <p>A sele\u00e7\u00e3o de pacientes para interven\u00e7\u00e3o \u00e9 baseada em v\u00e1rios fatores, incluindo tamanho do tumor, sintomas, risco de complica\u00e7\u00f5es e condi\u00e7\u00f5es associadas. Para angiomiolipomas pequenos (<4 cm) e assintom\u00e1ticos, normalmente \u00e9 recomendada vigil\u00e2ncia ativa com exames de imagem peri\u00f3dicos.<span class=\"citation\">2<\/span> Para tumores maiores, les\u00f5es sintom\u00e1ticas ou aqueles com alto risco de sangramento, a interven\u00e7\u00e3o pode ser necess\u00e1ria.<span class=\"citation\">5<\/span><\/p>\n <p>As op\u00e7\u00f5es de tratamento incluem:<\/p>\n <ul>\n <li>Vigil\u00e2ncia ativa com exames de imagem peri\u00f3dicos para tumores pequenos e assintom\u00e1ticos<\/li>\n <li>Emboliza\u00e7\u00e3o arterial seletiva para controle de sangramento ou redu\u00e7\u00e3o do tamanho do tumor<\/li>\n <li>Cirurgia preservadora de n\u00e9frons (nefrectomia parcial) para casos selecionados<\/li>\n <li>Terapia farmacol\u00f3gica com inibidores da rapamicina alvo em mam\u00edferos (mTOR), como sirolimus ou everolimus, particularmente para pacientes com complexo de esclerose tuberosa<span class=\"citation\">4<\/span><\/li><\/ul>\n <p>Para pacientes com complexo de esclerose tuberosa, recomenda-se o rastreamento de angiomiolipomas renais, pois esses pacientes geralmente desenvolvem m\u00faltiplos tumores bilaterais que podem exigir interven\u00e7\u00e3o precoce.<span class=\"citation\">1<\/span> Da mesma forma, pacientes com linfangioleiomiomatose devem ser submetidos a exames de imagem renais para rastreamento de angiomiolipomas.<span class=\"citation\">5<\/span><\/p>\n<p>De acordo com as diretrizes da EAU, angiomiolipomas menores que 4 cm s\u00e3o geralmente manejados com vigil\u00e2ncia ativa. Tumores maiores que 4 cm ou sintom\u00e1ticos t\u00eam risco aumentado de sangramento espont\u00e2neo e podem requerer emboliza\u00e7\u00e3o arterial seletiva ou nefrectomia parcial. Em pacientes com esclerose tuberosa, o uso de inibidores de mTOR (everolimus) \u00e9 uma op\u00e7\u00e3o terap\u00eautica reconhecida.<\/p>","gt-related-evidence":null,"gt-featured":true,"gt-ai-referenced":false,"gt-view-count":50},"yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v27.9 (Yoast SEO v27.9) - https:\/\/yoast.com\/product\/yoast-seo-premium-wordpress\/ -->\n<title>Angiomiolipoma Renal: Diagn\u00f3stico e Tratamento | Rigicon<\/title>\n<meta name=\"description\" content=\"Saiba sobre o angiomiolipoma renal, tumor benigno composto de gordura, m\u00fasculo e vasos. 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