{"id":12403,"date":"2025-08-01T12:42:47","date_gmt":"2025-08-01T16:42:47","guid":{"rendered":"https:\/\/www.rigicon.com\/glossary-term\/polycystic-kidney-disease\/"},"modified":"2026-03-22T06:33:07","modified_gmt":"2026-03-22T10:33:07","slug":"polycystic-kidney-disease","status":"publish","type":"glossary-term","link":"https:\/\/www.rigicon.com\/ko\/glossary-term\/polycystic-kidney-disease\/","title":{"rendered":"\ub2e4\ub0ad\uc131 \uc2e0\uc7a5 \uc9c8\ud658"},"content":{"rendered":"","protected":false},"excerpt":{"rendered":"","protected":false},"featured_media":0,"template":"","glossary-category":[126],"glossary-product":[],"class_list":["post-12403","glossary-term","type-glossary-term","status-publish","hentry","glossary-category-urological-conditions"],"acf":{"gt-definition":"<p>\ub2e4\ub0ad\uc131 \uc2e0\uc7a5 \uc9c8\ud658(PKD)\uc740 \uc2e0\uc7a5\uc5d0 \uccb4\uc561\uc774 \uac00\ub4dd \ucc2c \uc218\ub9ce\uc740 \ub0ad\uc885\uc774 \ubc1c\uc0dd\ud558\uc5ec \uc810\uc9c4\uc801\uc778 \uc2e0\uc7a5 \ube44\ub300\uc640 \uc810\uc9c4\uc801\uc778 \uc2e0\uc7a5 \uae30\ub2a5 \uc800\ud558\ub97c \ucd08\ub798\ud558\ub294 \uac83\uc774 \ud2b9\uc9d5\uc778 \uc720\uc804 \uc9c8\ud658\uc785\ub2c8\ub2e4.<sup>1<\/sup> \uc774\ub294 \ub450 \uac00\uc9c0 \uc77c\ucc28 \uc720\uc804 \ud615\ud0dc, \uc989 \uc0c1\uc5fc\uc0c9\uccb4 \uc6b0\uc131 \ub2e4\ub0ad\uc131 \uc2e0\uc7a5 \uc9c8\ud658(ADPKD)\uacfc \uc0c1\uc5fc\uc0c9\uccb4 \uc5f4\uc131 \ub2e4\ub0ad\uc131 \uc2e0\uc7a5 \uc9c8\ud658(ARPKD)\uc73c\ub85c \uc874\uc7ac\ud569\ub2c8\ub2e4.<sup>2<\/sup> ADPKD\ub294 \ub354 \ub9ce\uc740 \uac83\uc785\ub2c8\ub2e4. \uc77c\ubc18\uc801\uc73c\ub85c \uc804 \uc138\uacc4\uc801\uc73c\ub85c \uc57d 400~1,000\uba85 \uc911 1\uba85\uc5d0\uac8c \uc601\ud5a5\uc744 \ubbf8\uce58\ub294 \ubc18\uba74, ARPKD\ub294 \ub4dc\ubb3c\uac8c \ubc1c\uc0dd\ud558\uba70 \ucd9c\uc0dd\uc544 20,000~40,000\uba85 \uc911 \uc57d 1\uba85\uc5d0\uac8c \ubc1c\uc0dd\ud569\ub2c8\ub2e4.\u00a4<sup>3<\/sup><\/p>\n <p>ADPKD\ub294 \uc2e0\uc7a5 \ube44\ub300 \ubc0f \uc2ec\uc7a5, \uac04, \ucdcc\uc7a5, \ube44\uc7a5 \ubc0f \uac70\ubbf8\ub9c9\uacfc \uac19\uc740 \uc2e0\uc7a5 \uc678 \uae30\uad00 \uce68\ubc94\uacfc \uad00\ub828\ub41c \uc591\uce21\uc131 \uc2e0\uc7a5 \ub0ad\uc885\uc774 \uc788\ub294 \ub2e4\uacc4\ud1b5 \ubc0f \uc9c4\ud589\uc131 \uc720\uc804 \uc9c8\ud658\uc785\ub2c8\ub2e4. \uc774 \uc9c8\ubcd1\uc740 \uc8fc\ub85c \ub450 \uac00\uc9c0 \uc720\uc804\uc790\uc758 \ub3cc\uc5f0\ubcc0\uc774\uc5d0 \uc758\ud574 \ubc1c\uc0dd\ud569\ub2c8\ub2e4: \uc57d 85%\ub97c \ucc28\uc9c0\ud558\ub294 PKD1(\uc5fc\uc0c9\uccb4 16p13.3) \ubc0f PKD2 (4q21), \uc0ac\ub840\uc758 \uc57d 15%\uc5d0 \uae30\uc5ec\ud569\ub2c8\ub2e4.<sup>5<\/sup> \uc0ac\ub840\uc758 \uc791\uc740 \ube44\uc728(\uc57d 1%)\uc740 GANAB \uc720\uc804\uc790\uc758 \ub3cc\uc5f0\ubcc0\uc774\uc640 \uad00\ub828\ub418\uc5b4 \uc788\uc73c\uba70, \uc774\ub294 \uc2e0\uc7a5 \ud45c\ud604\ud615\uc774 \ub354 \uacbd\ubbf8\ud558\uc9c0\ub9cc \uac04 \uc9c8\ud658\uc774 \ub354 \ub450\ub4dc\ub7ec\uc9d1\ub2c8\ub2e4.<sup>6<\/sup><\/p>\n <p>PKD\uc758 \ubcd1\ud0dc\uc0dd\ub9ac\ud559\uc740 \uc2e0\uc7a5 \uc0c1\ud53c \uc138\ud3ec\uc758 \uc77c\ucc28 \uc12c\ubaa8\uc5d0 \uc874\uc7ac\ud558\uace0 \uc138\ud3ec \uc99d\uc2dd, \ubd84\ud654 \ubc0f \uccb4\uc561 \ubd84\ube44\uc5d0 \uc911\uc694\ud55c \uc5ed\ud560\uc744 \ud558\ub294 \ud3f4\ub9ac\uc2dc\uc2a4\ud2f4 \ub2e8\ubc31\uc9c8(PC1 \ubc0f PC2)\uc758 \ube44\uc815\uc0c1\uc801\uc778 \uae30\ub2a5\uacfc \uad00\ub828\ub429\ub2c8\ub2e4. \uc774 \ub2e8\ubc31\uc9c8\uc740 \uc138\ud3ec\ub0b4 \uce7c\uc298 \uc218\uc900\uacfc \uc21c\ud658 \uc544\ub370\ub178\uc2e0 \ubaa8\ub178\ud3ec\uc2a4\ud398\uc774\ud2b8(cAMP) \uc2e0\ud638 \uc804\ub2ec \uacbd\ub85c\ub97c \uc870\uc808\ud569\ub2c8\ub2e4. \uc774\ub7ec\ud55c \uacbd\ub85c\uc758 \uae30\ub2a5 \uc7a5\uc560\ub294 \uc8fc\ub85c \ub0ad\ud3ec\uc131 \uc12c\uc720\uc99d \ub9c9\ud6a1\ub2e8 \uc804\ub3c4\uccb4 \uc870\uc808\uae30(CFTR)\ub97c \ud1b5\ud574 \ub0b4\uac15 \ub9c9\uc744 \ud1b5\ud574 \uc5fc\ud654\ubb3c \ubd84\ube44\ub97c \uc99d\uac00\uc2dc\ucf1c \ub0ad\uc885 \ub0b4\uc5d0 \uccb4\uc561\uc774 \ucd95\uc801\ub418\uac8c \ud569\ub2c8\ub2e4.\u00a4<sup>8<\/sup><\/p>\n <p>\uc9c8\ubcd1\uc774 \uc9c4\ud589\ub428\uc5d0 \ub530\ub77c \ub0ad\uc885\uc758 \uc9c0\uc18d\uc801\uc778 \ud655\uc7a5\uc740 \uc2e0\uc7a5 \ud608\uad00\uc744 \uc555\ubc15\ud558\uc5ec \uc2e0\uc7a5 \ub0b4 \ud5c8\ud608\uc744 \uc720\ubc1c\ud558\uace0 \ub808\ub2cc-\uc548\uc9c0\uc624\ud150\uc2e0-\uc54c\ub3c4\uc2a4\ud14c\ub860 \uc2dc\uc2a4\ud15c\uc744 \ud65c\uc131\ud654\ud558\uc5ec \uace0\ud608\uc555(ADPKD\uc758 \uc77c\ubc18\uc801\uc778 \ucd08\uae30 \uc99d\uc0c1)\uc744 \uc720\ubc1c\ud569\ub2c8\ub2e4. \ub0ad\uc885\uc740 \ub610\ud55c \uc8fc\ubcc0 \uc2e0\uc7a5 \uc2e4\uc9c8\uc5d0\uc11c \uc5fc\uc99d \ubc18\uc751\uc744 \uc720\ubc1c\ud558\uc5ec \uc2e0\uc7a5 \uc12c\uc720\uc99d\uc744 \ucd09\uc9c4\ud569\ub2c8\ub2e4. \uc9c4\ud589\uc131 \ub0ad\uc885 \ud655\uc7a5, \uc99d\uac00\ub41c \uc804\uc2e0 \ud608\uad00 \uc800\ud56d, \ub098\ud2b8\ub968 \uc800\ub958 \ubc0f \uc9c4\ud589\uc131 \uc2e0\uc7a5 \uc12c\uc720\uc99d\uc740 \uad81\uadf9\uc801\uc73c\ub85c \ub9ce\uc740 \ud658\uc790\uc5d0\uc11c \ub9d0\uae30 \uc2e0\uc7a5 \uc9c8\ud658(ESKD)\uc73c\ub85c \uc774\uc5b4\uc9d1\ub2c8\ub2e4.\u00a4<sup>10<\/sup><\/p>\n <p>\uc784\uc0c1 \uc99d\uc0c1\uc740 \uc77c\ubc18\uc801\uc73c\ub85c ADPKD \ud658\uc790\uc758 30~40\ub300\uae4c\uc9c0 \ub098\ud0c0\ub098\uc9c0 \uc54a\ub294 \ubc18\uba74, ARPKD\ub294 \uc885\uc885 \ucd9c\uc0b0 \uc804\ud6c4 \ub610\ub294 \uc720\uc544\uae30\uc5d0 \ub354 \uc2ec\uac01\ud55c \uc99d\uc0c1\uc73c\ub85c \ub098\ud0c0\ub0a9\ub2c8\ub2e4.\u00a4<sup>11<\/sup> \uc77c\ubc18\uc801\uc778 \ud569\ubcd1\uc99d\uc73c\ub85c\ub294 \uace0\ud608\uc555, \uc2e0\uc7a5 \ud1b5\uc99d, \uc694\ub85c \uac10\uc5fc, \uc2e0\uc7a5 \uacb0\uc11d\uc774 \uc788\uc73c\uba70, \uacb0\uad6d\uc5d0\ub294 \ud22c\uc11d\uc774\ub098 \uc774\uc2dd\uc774 \ud544\uc694\ud55c \uc2e0\ubd80\uc804\uc774 \ubc1c\uc0dd\ud569\ub2c8\ub2e4.<sup>12<\/sup><\/p>\n<p>EAU \uc2e0\uc7a5\uc554 \uac00\uc774\ub4dc\ub77c\uc778\uc5d0\uc11c \ub2e4\ub0ad\uc131 \uc2e0\uc7a5 \uc9c8\ud658\uc740 \uc0c1\uc5fc\uc0c9\uccb4 \uc6b0\uc131(ADPKD, PKD1\/PKD2 \uc720\uc804\uc790)\uc774 \uac00\uc7a5 \ud754\ud558\uba70, \ub9d0\uae30 \uc2e0\ubd80\uc804\uc758 4\ubc88\uc9f8 \uc6d0\uc778\uc785\ub2c8\ub2e4. \ud1a8\ubc25\ud0c4(V2 \uc218\uc6a9\uccb4 \uae38\ud56d\uc81c)\uc774 ADPKD\uc758 \uc9c4\ud589\uc744 \ub2a6\ucd94\ub294 \uac83\uc73c\ub85c \uc785\uc99d\ub418\uc5c8\uc2b5\ub2c8\ub2e4 (EAU Renal Cell Carcinoma Guidelines, 2024).<\/p>","gt-synonyms":"ADPKD, \uc131\uc778 \ub2e4\ub0ad\uc131 \uc2e0\uc7a5 \uc9c8\ud658, \uc0c1\uc5fc\uc0c9\uccb4 \uc6b0\uc131 \ub2e4\ub0ad\uc131 \uc2e0\uc7a5 \uc9c8\ud658, PKD, ARPKD, \uc0c1\uc5fc\uc0c9\uccb4 \uc5f4\uc131 \ub2e4\ub0ad\uc131 \uc2e0\uc7a5 \uc9c8\ud658, \uc601\uc544 \ub2e4\ub0ad\uc131 \uc2e0\uc7a5 \uc9c8\ud658, \ud3ec\ud130 I\ud615 \ub2e4\ub0ad\uc131 \uc2e0\uc7a5 \uc9c8\ud658, \ub2e4\ub0ad\uc131 \uc2e0\uc7a5 \uc9c8\ud658","gt-citation":"[1] Bergmann C, Guay-Woodford LM, Harris PC, Horie S, Peters DJM, Torres VE. Polycystic kidney disease. Nat Rev Dis Primers. 2018 Dec 6;4(1):50. DOI: 10.1038\/s41572-018-0047-y\n\n[2] Mahboob M, Rout P, Leslie SW, Bokhari SRA. Autosomal Dominant Polycystic Kidney Disease. StatPearls [Internet]. 2024 Mar 20. PMID: 30523303\n\n[3] Harris PC, Torres VE. Polycystic kidney disease. Annu Rev Med. 2009;60:321-37. DOI: 10.1146\/annurev.med.60.101707.125712\n\n[4] Torres VE, Harris PC, Pirson Y. Autosomal dominant polycystic kidney disease. Lancet. 2007;369(9569):1287-1301. DOI: 10.1016\/S0140-6736(07)60601-1\n\n[5] Chebib FT, Torres VE. Autosomal Dominant Polycystic Kidney Disease: Core Curriculum 2016. Am J Kidney Dis. 2016;67(5):792-810. DOI: 10.1053\/j.ajkd.2015.07.037\n\n[6] Porath B, Gainullin VG, Cornec-Le Gall E, et al. Mutations in GANAB, Encoding the Glucosidase II\u03b1 Subunit, Cause Autosomal-Dominant Polycystic Kidney and Liver Disease. Am J Hum Genet. 2016;98(6):1193-1207. DOI: 10.1016\/j.ajhg.2016.05.004\n\n[7] Nauli SM, Alenghat FJ, Luo Y, et al. Polycystins 1 and 2 mediate mechanosensation in the primary cilium of kidney cells. Nat Genet. 2003;33(2):129-137. DOI: 10.1038\/ng1076\n\n[8] Hanaoka K, Qian F, Boletta A, et al. Co-assembly of polycystin-1 and -2 produces unique cation-permeable currents. Nature. 2000;408(6815):990-994. DOI: 10.1038\/35050128\n\n[9] Chapman AB, Johnson A, Gabow PA, Schrier RW. The renin-angiotensin-aldosterone system and autosomal dominant polycystic kidney disease. N Engl J Med. 1990;323(16):1091-1096. DOI: 10.1056\/NEJM199010183231602\n\n[10] Grantham JJ, Torres VE, Chapman AB, et al. Volume progression in polycystic kidney disease. N Engl J Med. 2006;354(20):2122-2130. DOI: 10.1056\/NEJMoa054341","gt-clinical-context":"<p>\ub2e4\ub0ad\uc131 \uc2e0\uc7a5 \uc9c8\ud658(PKD)\uc740 \ud658\uc790 \uad00\ub9ac, \uc120\ubcc4 \ubc0f \uce58\ub8cc\uc5d0 \uc911\uc694\ud55c \uc601\ud5a5\uc744 \ubbf8\uce58\ub294 \uc2e0\uc7a5\ud559 \uc2e4\uc2b5\uc5d0\uc11c \uc911\uc694\ud55c \uc784\uc0c1 \uacfc\uc81c\ub97c \ub098\ud0c0\ub0c5\ub2c8\ub2e4.\u00a4<sup>1<\/sup> PKD\uc758 \uc784\uc0c1\uc801 \ub9e5\ub77d\uc740 \uc9c8\ubcd1 \uc9c4\ud589\uc744 \ub2a6\ucd94\uace0 \uc2e0\uc7a5 \uae30\ub2a5\uc744 \ubcf4\uc874\ud558\ub294 \uac83\uc744 \ubaa9\ud45c\ub85c \ud558\ub294 \uc9c4\ub2e8, \uc9c8\ubcd1 \ubaa8\ub2c8\ud130\ub9c1, \ud569\ubcd1\uc99d \uad00\ub9ac \ubc0f \uce58\ub8cc \uc804\ub7b5\uc744 \ud3ec\ud568\ud569\ub2c8\ub2e4.<\/p>\n <p>ADPKD\uc758 \uc9c4\ub2e8\uc740 \uc77c\ubc18\uc801\uc73c\ub85c \uc601\uc0c1 \uc5f0\uad6c\ub97c \ud1b5\ud574 \uc774\ub8e8\uc5b4\uc9c0\uba70 \ucd08\uc74c\ud30c\ub294 \uc811\uadfc\uc131, \uc548\uc804\uc131 \ubc0f \ube44\uc6a9 \ud6a8\uc728\uc131\uc73c\ub85c \uc778\ud574 \uac00\uc7a5 \uc77c\ubc18\uc801\uc778 \ucd08\uae30 \ubc29\uc2dd\uc785\ub2c8\ub2e4.<sup>2<\/sup> \uc9c4\ub2e8 \uae30\uc900\uc740 \uc5f0\ub839\uc5d0 \ub530\ub77c \ub2e4\ub974\uba70, \uc80a\uc740 \ud658\uc790(15~39\uc138)\ub294 \ub178\uc778\ubcf4\ub2e4 \uc9c4\ub2e8\uc5d0 \ud544\uc694\ud55c \ub0ad\uc885\uc774 \ub354 \uc801\uc2b5\ub2c8\ub2e4.<sup>3<\/sup> \uc790\uae30\uacf5\uba85\uc601\uc0c1(MRI)\uacfc \ucef4\ud4e8\ud130 \ub2e8\uce35\ucd2c\uc601(CT)\uc740 \ub354 \uc791\uc740 \ub0ad\uc885\uc744 \ubc1c\uacac\ud558\ub294 \ub370 \ub354 \ub192\uc740 \uac10\ub3c4\ub97c \uc81c\uacf5\ud558\uba70 \uc885\uc885 \ub354 \ub9ce\uc740 \uc6a9\ub3c4\ub85c \uc0ac\uc6a9\ub429\ub2c8\ub2e4. \uc0c1\uc138\ud55c \ud3c9\uac00 \ub610\ub294 \ucd08\uc74c\ud30c \uacb0\uacfc\uac00 \ubaa8\ud638\ud55c \uacbd\uc6b0.<sup>4<\/sup> \ud2b9\ud788 \ube44\uc815\ud615 \ubc1c\ud604, \uc870\uae30 \ubc1c\ubcd1 \uc9c8\ubcd1\uc758 \uacbd\uc6b0 \ub610\ub294 \uac00\uc871 \uacc4\ud68d \ubaa9\uc801\uc73c\ub85c \uc720\uc804\uc790 \uac80\uc0ac\uac00 \uc810\uc810 \ub354 \ub9ce\uc774 \ud65c\uc6a9\ub418\uace0 \uc788\uc2b5\ub2c8\ub2e4.<sup>5<\/sup><\/p>\n <p>\uc9c8\ubcd1 \uc9c4\ud589 \ubaa8\ub2c8\ud130\ub9c1\uc740 PKD \uad00\ub9ac\uc5d0 \ud544\uc218\uc801\uc774\uba70, \ucd1d \uc2e0\uc7a5 \uc6a9\uc801(TKV)\uc774 \uc9c8\ubcd1 \uc9c4\ud589\uc758 \uac00\uc7a5 \uc2e0\ub8b0\ud560 \uc218 \uc788\ub294 \ubc14\uc774\uc624\ub9c8\ucee4\ub85c \ub5a0\uc624\ub974\uace0 \uc788\uc2b5\ub2c8\ub2e4.<sup>6<\/sup> Mayo \ubd84\ub958 \uc2dc\uc2a4\ud15c(\ud074\ub798\uc2a4 1A, 1B, 1C, 1D \ubc0f 1E)\uc740 \uc9c8\ubcd1 \uacb0\uacfc\uac00 \ub354 \ub098\ube60\uc9c8 \uc704\ud5d8\uc774 \uac00\uc7a5 \ub0ae\uc740 \uac83\ubd80\ud130 \uac00\uc7a5 \ub192\uc740 \uac83\uae4c\uc9c0 \ud658\uc790\ub97c \ubd84\ub958\ud558\uba70, \ub9c8\uc9c0\ub9c9 3\ub2e8\uacc4\ub294 \ub9d0\uae30 \uc2e0\uc7a5 \uc9c8\ud658\uc758 \ub354 \ub192\uc740 \uc704\ud5d8\uacfc \uc5f0\uad00\ub429\ub2c8\ub2e4 (ESKD).\u00a4\u00a4<sup>7<\/sup> \uc774 \ubd84\ub958\ub294 \ubcf4\ub2e4 \uacf5\uaca9\uc801\uc778 \uad00\ub9ac \uc811\uadfc \ubc29\uc2dd\uc73c\ub85c \ud61c\ud0dd\uc744 \ubcfc \uc218 \uc788\ub294 \uace0\uc704\ud5d8 \ud658\uc790\ub97c \uc2dd\ubcc4\ud558\ub294 \ub370 \ub3c4\uc6c0\uc774 \ub429\ub2c8\ub2e4.<\/p>\n <p>\uace0\ud608\uc555\uc740 ADPKD\uc758 \uc77c\ubc18\uc801\uc778 \ucd08\uae30 \uc99d\uc0c1\uc73c\ub85c, \uc885\uc885 \uc2e0\uc7a5 \uae30\ub2a5\uc758 \uc0c1\ub2f9\ud55c \uc800\ud558\uc5d0 \uc120\ud589\ud558\uba70, \ub354 \ube60\ub978 \uc9c8\ubcd1 \uc9c4\ud589 \ubc0f \uc2ec\ud608\uad00 \uc774\ud658\uc728 \uc99d\uac00\uc640 \uad00\ub828\uc774 \uc788\uc2b5\ub2c8\ub2e4.<sup>8<\/sup> \ud608\uc555 \uc870\uc808\uc740 ADPKD \uad00\ub9ac\uc758 \ucd08\uc11d\uc774\uba70 \uad8c\uc7a5\ub418\ub294 \ubaa9\ud45c\uce58\ub294 130\/80mmHg \ubbf8\ub9cc\uc785\ub2c8\ub2e4.<sup>9<\/sup> \uc548\uc9c0\uc624\ud150\uc2e0 \uc804\ud658 \ud6a8\uc18c \uc5b5\uc81c\uc81c(ACEI) \ubc0f \uc548\uc9c0\uc624\ud150\uc2e0 \uc218\uc6a9\uccb4 \ucc28\ub2e8\uc81c (ARB)\ub294 \ud608\uc555 \uc870\uc808 \uc774\uc0c1\uc758 \uc7a0\uc7ac\uc801 \uc2e0\uc7a5 \ubcf4\ud638 \ud6a8\uacfc\ub85c \uc778\ud574 \uc120\ud638\ub418\ub294 \ud56d\uace0\ud608\uc555\uc81c\uc785\ub2c8\ub2e4.<sup>10<\/sup><\/p>\n <p>\ub9ce\uc740 \ud658\uc790\uac00 \ub0ad\uc885 \ube44\ub300, \uac10\uc5fc \ub610\ub294 \uc2e0\uc7a5 \uacb0\uc11d\uacfc \uad00\ub828\ub41c \uae09\uc131 \ub610\ub294 \ub9cc\uc131 \ud1b5\uc99d\uc744 \uacbd\ud5d8\ud558\ubbc0\ub85c \ud1b5\uc99d \uad00\ub9ac\ub294 \ub2e4\ub0ad\uc2e0\uc7a5\ubcd1 \uce58\ub8cc\uc758 \ub610 \ub2e4\ub978 \uc911\uc694\ud55c \uce21\uba74\uc785\ub2c8\ub2e4.<sup>11<\/sup> \uce58\ub8cc \uc811\uadfc\ubc95\uc740 \ubcf4\uc874\uc801 \uc870\uce58(\uc9c4\ud1b5\uc81c, \uc0bc\ud658\uacc4 \ud56d\uc6b0\uc6b8\uc81c)\ubd80\ud130 \uc2ec\uac01\ud55c \uacbd\uc6b0 \uc911\uc7ac\uc801 \uc2dc\uc220(\ub0ad\ud3ec \ud761\uc778, \ubcf5\uac15\uacbd \ub0ad\ud3ec \ucc9c\uacf5)\uae4c\uc9c0 \ub2e4\uc591\ud569\ub2c8\ub2e4.<sup>12<\/sup><\/p>\n <p>\ub0ad\ud3ec \uac10\uc5fc\uc740 \ud50c\ub8e8\uc624\ub85c\ud034\ub180\ub860, \ud2b8\ub9ac\uba54\ud1a0\ud504\ub9bc-\uc124\ud30c\uba54\ud1a1\uc0ac\uc878, \ud074\ub9b0\ub2e4\ub9c8\uc774\uc2e0 \ub4f1 \ub0ad\ud3ec \uce68\ud22c\uac00 \uc88b\uc740 \ud56d\uc0dd\uc81c\ub85c \uc989\uac01\uc801\uc778 \uce58\ub8cc\uac00 \ud544\uc694\ud569\ub2c8\ub2e4.\u00a4<sup>13<\/sup> \uc9c0\uc18d\uc801\uc778 \uac10\uc5fc\uc73c\ub85c \uc778\ud574 \ub0ad\ud3ec \ubc30\uc561\uc774 \ud544\uc694\ud560 \uc218 \uc788\uc73c\uba70, \ub9d0\uae30\uc758 \uacbd\uc6b0 \uc2e0\uc7a5\uc808\uc81c\uc220\uc774 \ud544\uc694\ud560 \uc218 \uc788\uc2b5\ub2c8\ub2e4.<sup>14<\/sup><\/p>\n <p>\uc2e0\uacb0\uc11d\uc99d\uc740 ADPKD \ud658\uc790\uc758 \uc57d 20%\uc5d0\uc11c \ubc1c\uc0dd\ud558\uba70 \uc694\uc0b0 \uacb0\uc11d\uc774 \uac00\uc7a5 \ud754\ud558\uace0 \uc625\uc0b4\uc0b0\uce7c\uc298 \uacb0\uc11d\uc774 \uadf8 \ub4a4\ub97c \uc787\uc2b5\ub2c8\ub2e4.<sup>15<\/sup> \uad00\ub9ac\uc5d0\ub294 \uc218\ubd84 \uc12d\ucde8 \uc99d\uac00, \uad6c\uc5f0\uc0b0 \uce7c\ub968\uc744 \uc0ac\uc6a9\ud55c \uc18c\ubcc0 \uc54c\uce7c\ub9ac\ud654(\ud2b9\ud788 \uc694\uc0b0 \uacb0\uc11d\uc758 \uacbd\uc6b0), \ud544\uc694\ud55c \uacbd\uc6b0 \ud45c\uc900 \uc911\uc7ac \uc811\uadfc\ubc95\uc774 \ud3ec\ud568\ub429\ub2c8\ub2e4.<sup>16<\/sup><\/p>\n <p>\ubc14\uc18c\ud504\ub808\uc2e0 V2 \uc218\uc6a9\uccb4 \uae38\ud56d\uc81c\uc778 \ud1a8\ubc25\ud0c4\uc740 ADPKD \ud2b9\uc774\uc801 \uce58\ub8cc\ubc95\uc5d0\uc11c \uc0c1\ub2f9\ud55c \ubc1c\uc804\uc744 \ub098\ud0c0\ub0c5\ub2c8\ub2e4.<sup>17<\/sup> \uc784\uc0c1 \uc2dc\ud5d8\uc744 \ud1b5\ud574 TKV \uc99d\uac00 \ubc0f \ucd94\uc815 \uc0ac\uad6c\uccb4 \uc5ec\uacfc\uc728(eGFR) \uac10\uc18c\ub97c \ub2a6\ucd94\ub294 \ud6a8\ub2a5\uc774 \uc785\uc99d\ub418\uc5c8\uc2b5\ub2c8\ub2e4.<sup>18<\/sup> \uadf8\ub7ec\ub098 \uc774 \uc81c\ud488\uc744 \uc0ac\uc6a9\ud558\ub824\uba74 \uc2e0\uc911\ud55c \ud658\uc790 \uc120\ud0dd, \uc7a0\uc7ac\uc801\uc778 \uac04\ub3c5\uc131\uc5d0 \ub300\ud55c \ubaa8\ub2c8\ud130\ub9c1, \ub2e4\ub1e8\uc99d \ubc0f \ub2e4\ub1e8\uc99d\uacfc \uac19\uc740 \ubd80\uc791\uc6a9 \uad00\ub9ac\uac00 \ud544\uc694\ud569\ub2c8\ub2e4. \ub2e4\uac08\uc99d.<sup>19<\/sup><\/p>\n <p>\ubc14\uc18c\ud504\ub808\uc2e0\uc744 \uc5b5\uc81c\ud558\uace0 cAMP \uc0dd\uc131\uc744 \uac10\uc18c\uc2dc\ud0a4\uae30 \uc704\ud55c \uc218\ubd84 \uc12d\ucde8 \uc99d\uac00(\ub9e4\uc77c \ucd5c\uc18c 3\ub9ac\ud130), \ub098\ud2b8\ub968 \uc81c\ud55c(\ub9e4\uc77c 2g \ubbf8\ub9cc) \ubc0f \uaddc\uce59\uc801\uc778 \uc2e0\uccb4 \ud65c\ub3d9\uc744 \ud3ec\ud568\ud558\uc5ec \ubaa8\ub4e0 PKD \ud658\uc790\uc5d0\uac8c \uc0dd\ud65c \ubc29\uc2dd \uc218\uc815\uc774 \uad8c\uc7a5\ub429\ub2c8\ub2e4.\u00a4<sup>20<\/sup><\/p>\n <p>ESKD\ub85c \uc9c4\ud589\ub418\ub294 \ud658\uc790\uc758 \uacbd\uc6b0 \uc2e0\uc7a5 \ub300\uccb4 \uc694\ubc95 \uc635\uc158\uc5d0\ub294 \ud22c\uc11d\uacfc \uc2e0\uc7a5 \uc774\uc2dd\uc774 \ud3ec\ud568\ub418\uba70, \ud6c4\uc790\ub294 \uc801\ud569\ud55c \ud6c4\ubcf4\uc790\uc5d0\uac8c \uc6b0\uc218\ud55c \uacb0\uacfc\ub97c \uc81c\uacf5\ud569\ub2c8\ub2e4.<sup>21<\/sup> \uc2e0\uc7a5\uc774 \ub300\ub7c9\uc73c\ub85c \ucee4\uc838 \uc2ec\uac01\ud55c \uc99d\uc0c1\uc744 \uc720\ubc1c\ud558\uac70\ub098 \uc774\uc2dd\uc744 \uc704\ud55c \uacf5\uac04\uc744 \ud655\ubcf4\ud558\uae30 \uc704\ud574 \uc2e0\uc7a5\uc808\uc81c\uc220\uc774 \ud544\uc694\ud560 \uc218 \uc788\uc2b5\ub2c8\ub2e4.<sup>22<\/sup><\/p>\n <p>\uc720\uc804 \uc0c1\ub2f4\uc740 PKD \ud658\uc790\uc640 \uadf8 \uac00\uc871\uc744 \uc704\ud55c \uce58\ub8cc\uc758 \uc911\uc694\ud55c \uad6c\uc131 \uc694\uc18c\ub85c\uc11c \uc720\uc804 \ud328\ud134, \uc7ac\ubc1c \uc704\ud5d8 \ubc0f \uc0dd\uc2dd \uc635\uc158\uc5d0 \ub300\ud55c \uc815\ubcf4\ub97c \uc81c\uacf5\ud569\ub2c8\ub2e4.\u00a4<sup>23<\/sup> \ucc29\uc0c1 \uc804 \uc720\uc804 \uc9c4\ub2e8\uc740 \uccb4\uc678 \uc218\uc815\uc744 \ubc1b\ub294 \ubd80\ubd80\uc5d0\uac8c PKD \ub3cc\uc5f0\ubcc0\uc774\uac00 \uc5c6\ub294 \ubc30\uc544\ub97c \uc120\ud0dd\ud560 \uac00\ub2a5\uc131\uc744 \uc81c\uacf5\ud569\ub2c8\ub2e4.\u00a4<sup>24<\/sup><\/p>\n<p>\ud55c\uad6d\uc5d0\uc11c ADPKD \uc720\ubcd1\ub960\uc740 \uc57d 1\/500-1\/1000\uc774\uba70, \ud3c9\uade0 50-60\ub300\uc5d0 \ub9d0\uae30 \uc2e0\ubd80\uc804\uc5d0 \ub3c4\ub2ec\ud569\ub2c8\ub2e4. \ub300\ud55c\uc2e0\uc7a5\ud559\ud68c\uc5d0\uc11c\ub294 \uc815\uae30\uc801\uc778 \uc2e0\uae30\ub2a5 \uac80\uc0ac, \ud608\uc555 \uad00\ub9ac, \ud1a8\ubc25\ud0c4 \uce58\ub8cc\ub97c \uad8c\uace0\ud569\ub2c8\ub2e4.<\/p>","gt-related-evidence":null,"gt-featured":true,"gt-ai-referenced":false,"gt-view-count":80},"yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v27.9 (Yoast SEO v27.9) - https:\/\/yoast.com\/product\/yoast-seo-premium-wordpress\/ -->\n<title>\ub2e4\ub0ad\uc131 \uc2e0\uc7a5 \uc9c8\ud658 | \uc720\uc804, \uc9c4\ub2e8, \ud1a8\ubc25\ud0c4 \uce58\ub8cc - Rigicon \uc6a9\uc5b4\uc9d1<\/title>\n<meta name=\"description\" content=\"\ub2e4\ub0ad\uc131 \uc2e0\uc7a5 \uc9c8\ud658\uc740 \uc2e0\uc7a5\uc5d0 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