{"id":12364,"date":"2025-07-22T08:25:02","date_gmt":"2025-07-22T12:25:02","guid":{"rendered":"https:\/\/www.rigicon.com\/glossary-term\/amino-aciduria\/"},"modified":"2026-03-22T06:32:12","modified_gmt":"2026-03-22T10:32:12","slug":"amino-aciduria","status":"publish","type":"glossary-term","link":"https:\/\/www.rigicon.com\/ko\/glossary-term\/amino-aciduria\/","title":{"rendered":"\uc544\ubbf8\ub178\uc0b0\ub1e8"},"content":{"rendered":"","protected":false},"excerpt":{"rendered":"","protected":false},"featured_media":0,"template":"","glossary-category":[126],"glossary-product":[108,107],"class_list":["post-12364","glossary-term","type-glossary-term","status-publish","hentry","glossary-category-urological-conditions","glossary-product-conticlassic-aus","glossary-product-contireflex-enhanced-aus"],"acf":{"gt-definition":"<p>\uc544\ubbf8\ub178\uc0b0\ub1e8\uc99d\uc740 \uc18c\ubcc0\uc5d0 \uc544\ubbf8\ub178\uc0b0\uc774 \uacfc\ub3c4\ud558\uac8c \uc874\uc7ac\ud558\ub294 \uac83\uc744 \uc758\ubbf8\ud558\uba70 \uc885\uc885 \ub300\uc0ac \uc7a5\uc560\ub97c \ub098\ud0c0\ub0c5\ub2c8\ub2e4.<sup>1<\/sup> \uc774 \uc9c8\ud658\uc740 \uc18c\ubcc0\uc5d0 \uccb4\ub0b4 \ub2e8\ubc31\uc9c8\uc758 \uad6c\uc131 \uc694\uc18c\uc778 \uc544\ubbf8\ub178\uc0b0\uc774 \ube44\uc815\uc0c1\uc801\uc73c\ub85c \ub9ce\uc774 \ud3ec\ud568\ub418\uc5b4 \uc788\uc744 \ub54c \ubc1c\uc0dd\ud569\ub2c8\ub2e4.<sup>2<\/sup> \uac74\uac15\ud55c \uc2e0\uc7a5\uc5d0\uc11c\ub294 \uc0ac\uad6c\uccb4\ub294 \ud608\uc561\uc5d0\uc11c \ubaa8\ub4e0 \uc544\ubbf8\ub178\uc0b0\uc744 \uac78\ub7ec\ub0b4\uace0 \uc2e0\uc7a5 \uc138\ub1e8\uad00\uc740 \uac78\ub7ec\uc9c4 \uc544\ubbf8\ub178\uc0b0\uc758 95% \uc774\uc0c1\uc744 \uc7ac\ud761\uc218\ud569\ub2c8\ub2e4. \uc0b0\uc740 \ud608\uc561\uc73c\ub85c \ub2e4\uc2dc \ub4e4\uc5b4\uac11\ub2c8\ub2e4.\u00a4<sup>3<\/sup><\/p>\n\n <p>\uc544\ubbf8\ub178\uc0b0\ub1e8\uc99d\uc740 \uae30\ubcf8 \uba54\ucee4\ub2c8\uc998\uc5d0 \ub530\ub77c \ub450 \uac00\uc9c0 \uc8fc\uc694 \uc720\ud615\uc73c\ub85c \ubd84\ub958\ub420 \uc218 \uc788\uc2b5\ub2c8\ub2e4.<\/p>\n\n <p>1. <strong>\uc544\ubbf8\ub178\uc0b0\ub1e8 \uacfc\uc789\uc99d<\/strong>: \ud608\uc7a5 \ub0b4 \ube44\uc815\uc0c1\uc801\uc73c\ub85c \ub192\uc740 \uc544\ubbf8\ub178\uc0b0 \ub18d\ub3c4\uac00 \uc2e0\uc7a5 \uc138\ub1e8\uad00\uc758 \ud761\uc218 \ub2a5\ub825\uc744 \uc555\ub3c4\ud558\uc5ec \uc18c\ubcc0 \ub0b4 \uc544\ubbf8\ub178\uc0b0 \ub18d\ub3c4\uac00 \ub192\uc544\uc9c0\ub294 \uacbd\uc6b0\uc5d0 \ubc1c\uc0dd\ud569\ub2c8\ub2e4.\u00a4<sup>4<\/sup> \uc774\ub294 \ud398\ub2d0\ucf00\ud1a4\ub1e8\uc99d\uacfc \uac19\uc740 \uc120\ucc9c\uc131 \uc544\ubbf8\ub178\uc0b0 \ub300\uc0ac \uc7a5\uc560\ub85c \uc778\ud574 \ubc1c\uc0dd\ud560 \uc218 \uc788\uac70\ub098 \uac04\uc5d0\uc11c \uc774\ucc28\uc801\uc73c\ub85c \ubc1c\uc0dd\ud560 \uc218 \uc788\uc2b5\ub2c8\ub2e4. \uc9c8\ubcd1.<sup>3<\/sup><\/p>\n\n <p>2. <strong>\uc2e0\uc7a5 \uc544\ubbf8\ub178\uc0b0\ub1e8\uc99d<\/strong>: \uc2e0\uc7a5 \uc138\ub1e8\uad00\uc774 \uc5ec\uacfc\ub41c \uc544\ubbf8\ub178\uc0b0\uc744 \ub2e4\uc2dc \ud608\uc561\uc73c\ub85c \uc7ac\ud761\uc218\ud560 \uc218 \uc5c6\uc5b4 \uc18c\ubcc0\uc5d0 \uc544\ubbf8\ub178\uc0b0 \ub18d\ub3c4\uac00 \ub192\uc544\uc9c8 \ub54c \ubc1c\uc0dd\ud569\ub2c8\ub2e4.\u00a4<sup>5<\/sup> \uc774\ub294 \ud558\ub974\ud2b8\ub204\ud504\ubcd1\uc5d0\uc11c \ubc1c\uc0dd\ud558\ub294 \uac83\ucc98\ub7fc \uc2e0\uc138\ub1e8\uad00\uc758 \uc218\uc1a1 \ub2e8\ubc31\uc9c8 \uacb0\ud568\uc73c\ub85c \uc778\ud574 \ubc1c\uc0dd\ud560 \uc218 \uc788\uac70\ub098 \ud310\ucf54\ub2c8\uc5d0\uc11c \ubc1c\uc0dd\ud558\ub294 \uac83\ucc98\ub7fc \uc2e0\uc7a5 \uc138\uad00 \uc190\uc0c1\uc73c\ub85c \uc778\ud574 \ubc1c\uc0dd\ud560 \uc218 \uc788\uc2b5\ub2c8\ub2e4. \uc99d\ud6c4\uad70.<sup>4<\/sup><\/p>\n\n <p>\uc720\uc804\uc131 \uc544\ubbf8\ub178\uc0b0\ub1e8\uc99d\uc740 \uc2e0\uc7a5\uc744 \ud1b5\ud55c \uc544\ubbf8\ub178\uc0b0 \uc218\uc1a1(\uc7ac\ud761\uc218) \ubc0f \ub9ce\uc740 \uacbd\uc6b0 \uc18c\uc7a5 \uc0c1\ud53c(\ud761\uc218)\ub97c \ud1b5\ud55c \uc544\ubbf8\ub178\uc0b0 \uc218\uc1a1 \uacb0\ud568\uc73c\ub85c \uc778\ud574 \ubc1c\uc0dd\ud569\ub2c8\ub2e4.\u00a4<sup>6<\/sup> \uc774\ub7ec\ud55c \uc7a5\uc560\ub294 \ud2b9\uc815 \uc544\ubbf8\ub178\uc0b0\uc774\ub098 \uc544\ubbf8\ub178\uc0b0 \uadf8\ub8f9\uc758 \ub300\uc0ac\uc5d0 \uc601\ud5a5\uc744 \ubbf8\uccd0 \ud608\uc561\uc5d0 \ucd95\uc801\ub41c \ud6c4 \uc18c\ubcc0\uc73c\ub85c \ubc30\uc124\ub420 \uc218 \uc788\uc2b5\ub2c8\ub2e4.<sup>7<\/sup><\/p> <p>\uc544\ubbf8\ub178\uc0b0\ub1e8\ub294 \uc18c\ubcc0\uc5d0\uc11c \ube44\uc815\uc0c1\uc801\uc73c\ub85c \ub9ce\uc740 \uc544\ubbf8\ub178\uc0b0\uc774 \ubc30\uc124\ub418\ub294 \uc0c1\ud0dc\ub85c, \uc2e0\uc138\uad00 \uae30\ub2a5 \uc7a5\uc560\ub97c \uc2dc\uc0ac\ud569\ub2c8\ub2e4. \uc720\ubcd1\ub960\uc740 \uc77c\ubc18 \uc778\uad6c\uc5d0\uc11c \uc57d 1\/10,000\uc774\uba70, \uc2dc\uc2a4\ud2f4\ub1e8\uc99d\uc774 \uac00\uc7a5 \ud754\ud55c \uc784\uc0c1\uc801\uc73c\ub85c \uc720\uc758\ubbf8\ud55c \ud615\ud0dc\uc785\ub2c8\ub2e4. EAU \uac00\uc774\ub4dc\ub77c\uc778\uc5d0\uc11c\ub294 \uc7ac\ubc1c\uc131 \uc694\ub85c\uacb0\uc11d \ud658\uc790\uc758 \ub300\uc0ac \ud3c9\uac00 \uc2dc \uc544\ubbf8\ub178\uc0b0\ub1e8 \uac80\uc0ac\ub97c \uad8c\uc7a5\ud569\ub2c8\ub2e4.<\/p>","gt-synonyms":"\uc544\ubbf8\ub178\uc0b0 - \uc18c\ubcc0, \uc18c\ubcc0 \uc544\ubbf8\ub178\uc0b0, \uace0\uc544\ubbf8\ub178\uc0b0\ub1e8\uc99d, \uc544\ubbf8\ub178\uc0b0\uc99d, \uc2e0\uc7a5 \uc544\ubbf8\ub178\uc0b0\ub1e8\uc99d, \uacfc\uc789 \uc544\ubbf8\ub178\uc0b0\ub1e8\uc99d, \uc804\uc2e0\uc131 \uc544\ubbf8\ub178\uc0b0\ub1e8\uc99d","gt-citation":"[1] Aliu E, Kanungo S, Arnold GL. Amino acid disorders. Ann Transl Med. 2018 Dec;6(24):471. DOI: 10.21037\/atm.2018.12.12\n\n[2] \"Aminoaciduria\". Mosby's Medical Dictionary (9th ed.). Mosby. 2013. p. 79. ISBN 9780323112581.\n\n[3] Sch\u00fcck, O (1984). \"Amino acids excretion. Physiology and pathophysiology\". Examination of Kidney Function. Translated by Cort, JH. Dordrecht: Springer Netherlands. p. 252. ISBN 9789400956605.\n\n[4] Crook, Martin Andrew (2012). \"Chapter 27: Inborn errors of metabolism\". Clinical biochemistry and metabolic medicine (8th ed.). London: Hodder Arnold. pp. 371\u2013383. ISBN 9781444144154.\n\n[5] Mundt, LA; Shanahan, K (2011). \"Chapter 7: Urinary and metabolic diseases and related urinalysis findings. Aminoacidurias\". Graff's textbook of routine urinalysis and body fluids (2nd ed.). Philadelphia: Wolters Kluwer\/Lippincott Williams & Wilkins Health. pp. 203\u2013210. ISBN 9781582558752.\n\n[6] \"Aminoaciduria\". ScienceDirect Topics. Retrieved from Kidney International, 2015. https:\/\/www.sciencedirect.com\/topics\/medicine-and-dentistry\/aminoaciduria\n\n[7] Ziegler SG, Ferreira CR. Inborn errors of amino acid metabolism. Transl Sci Rare Dis. 2023;6(1-2):37-55. DOI: 10.3233\/TRD-230018","gt-clinical-context":"<p>\uc544\ubbf8\ub178\uc0b0\ub1e8\uc99d\uc740 \ub2e4\uc591\ud55c \ub300\uc0ac \uc7a5\uc560, \ud2b9\ud788 \uc120\ucc9c\uc131 \uc544\ubbf8\ub178\uc0b0 \ub300\uc0ac \uc774\uc0c1\uc5d0 \ub300\ud55c \ubc14\uc774\uc624\ub9c8\ucee4 \uc5ed\ud560\uc744 \ud558\ub294 \uacbd\uc6b0\uac00 \ub9ce\uae30 \ub54c\ubb38\uc5d0 \uc784\uc0c1\uc801\uc73c\ub85c \uc911\uc694\ud569\ub2c8\ub2e4.<sup>1<\/sup> \uc784\uc0c1 \uc2e4\ubb34\uc5d0\uc11c \uc544\ubbf8\ub178\uc0b0\ub1e8\uc99d\uc740 \uc18c\ubcc0 \uc544\ubbf8\ub178\uc0b0 \ubd84\uc11d\uc744 \ud1b5\ud574 \uac80\ucd9c\ub429\ub2c8\ub2e4. \uc774 \ubd84\uc11d\uc740 \uc77c\ubc18\uc801\uc73c\ub85c \uc784\uc0c1 \uc99d\uc0c1\uc744 \uae30\ubc18\uc73c\ub85c \ub300\uc0ac \uc7a5\uc560\uac00 \uc758\uc2ec\ub418\uac70\ub098 \uc2e0\uc0dd\uc544 \uc120\ubcc4\uac80\uc0ac \ud6c4\uc18d \uc870\uce58\uc758 \uc77c\ubd80\ub85c \uc218\ud589\ub429\ub2c8\ub2e4.<sup>7<\/sup><\/p>\n\n <p>\uc544\ubbf8\ub178\uc0b0\ub1e8\uc99d\uc758 \uc784\uc0c1\uc801 \uc911\uc694\uc131\uc740 \uadfc\ubcf8 \uc6d0\uc778\uc5d0 \ub530\ub77c \ub2e4\ub985\ub2c8\ub2e4.<\/p>\n\n <p>1. <strong>\uc9c4\ub2e8\uc801 \uac00\uce58<\/strong>: \uc544\ubbf8\ub178\uc0b0\ub1e8\uc99d \ud328\ud134\uc740 \ud2b9\uc815 \ub300\uc0ac \uc7a5\uc560\ub97c \uc2dd\ubcc4\ud558\ub294 \ub370 \ub3c4\uc6c0\uc774 \ub420 \uc218 \uc788\uc2b5\ub2c8\ub2e4. \uc608\ub97c \ub4e4\uc5b4, \ud398\ub2d0\ucf00\ud1a4\ub1e8\uc99d(PKU)\uc740 \ud608\uc561\uacfc \uc18c\ubcc0 \ubaa8\ub450\uc5d0\uc11c \ud398\ub2d0\uc54c\ub77c\ub2cc\uc774 \uc99d\uac00\ud558\ub294 \uac83\uc774 \ud2b9\uc9d5\uc785\ub2c8\ub2e4.\u00a4<sup>1<\/sup> \ub9c8\ucc2c\uac00\uc9c0\ub85c, \uba54\uc774\ud50c \uc2dc\ub7fd \uc18c\ubcc0 \uc9c8\ud658\uc740 \ub192\uc740 \ubd84\uc9c0\uc1c4 \uc544\ubbf8\ub178\uc0b0\uc744 \ub098\ud0c0\ub0c5\ub2c8\ub2e4.\u00a4<sup>7<\/sup><\/p>\n\n <p>2. <strong>\ud658\uc790 \uc120\ud0dd \uae30\uc900<\/strong>: \uc18c\ubcc0 \uc544\ubbf8\ub178\uc0b0 \uac80\uc0ac\uac00 \ud544\uc694\ud560 \uc218 \uc788\ub294 \ud658\uc790\uc5d0\ub294 \uc124\uba85\ud560 \uc218 \uc5c6\ub294 \ubc1c\ub2ec \uc9c0\uc5f0, \uc2e0\uacbd\ud559\uc801 \uc99d\uc0c1, \ud2b9\uc774\ud55c \ub0c4\uc0c8, \uc131\uc7a5 \uc7a5\uc560, \ub300\uc0ac \uc7a5\uc560 \uac00\uc871\ub825\uc774 \uc788\ub294 \ud658\uc790\uac00 \ud3ec\ud568\ub429\ub2c8\ub2e4.\u00a4<sup>5<\/sup><\/p>\n\n <p>3. <strong>\uc784\uc0c1 \uad00\ub9ac<\/strong>: \ub9ce\uc740 \uc544\ubbf8\ub178\uc0b0 \uc7a5\uc560\uc758 \uacbd\uc6b0 \ubb38\uc81c\uac00 \ub418\ub294 \uc544\ubbf8\ub178\uc0b0\uc5d0 \ub300\ud55c \uc2dd\uc774 \uc81c\ud55c\uc774 \uce58\ub8cc\uc758 \uc911\uc2ec\uc785\ub2c8\ub2e4.\u00a4<sup>1<\/sup> \uc774\ub7ec\ud55c \uc811\uadfc\ubc95\uc740 \"\ub300\uc0ac \uc601\uc591' \ubd84\uc57c\uc758 \ubc1c\uc804\uc73c\ub85c \uc774\uc5b4\uc84c\uc2b5\ub2c8\ub2e4.\u00a4<sup>1<\/sup> \uc608\ub97c \ub4e4\uc5b4, PKU\uc5d0\uc11c\ub294 \ud398\ub2d0\uc54c\ub77c\ub2cc \uc81c\ud55c \uc2dd\uc774\uc694\ubc95\uc774 \uc2dc\uc791\ub418\uc5c8\uc744 \ub54c \uc9c0\uc801 \uc7a5\uc560\ub97c \uc608\ubc29\ud558\ub294 \ub370 \uc131\uacf5\ud588\uc2b5\ub2c8\ub2e4. \uc77c\ucc0d.<sup>1<\/sup><\/p>\n\n <p>4. <strong>\uae30\ub300 \uacb0\uacfc<\/strong>: \uc544\ubbf8\ub178\uc0b0 \uc7a5\uc560\uc758 \uc870\uae30 \uc9c4\ub2e8\uacfc \uc801\uc808\ud55c \uad00\ub9ac\ub294 \uacb0\uacfc\ub97c \ud06c\uac8c \uac1c\uc120\ud560 \uc218 \uc788\uc2b5\ub2c8\ub2e4. \uce58\ub8cc\ud558\uc9c0 \uc54a\uc73c\uba74 \uc774\ub7ec\ud55c \uc7a5\uc560 \uc911 \ub2e4\uc218\uac00 \uc9c0\uc801 \uc7a5\uc560, \ubc1c\ub2ec \uc9c0\uc5f0, \uc2e0\uacbd\ud559\uc801 \uc190\uc0c1\uc73c\ub85c \uc774\uc5b4\uc9c8 \uc218 \uc788\uc73c\uba70 \uc5b4\ub5a4 \uacbd\uc6b0\uc5d0\ub294 \uc0ac\ub9dd\uc5d0 \uc774\ub97c \uc218\ub3c4 \uc788\uc2b5\ub2c8\ub2e4.\u00a4<sup>1<\/sup> \uadf8\ub7ec\ub098 \uc801\uc808\ud55c \uad00\ub9ac\ub97c \ud1b5\ud574 \ub9ce\uc740 \ud658\uc790\uac00 \ube44\uad50\uc801 \uc815\uc0c1\uc801\uc778 \uc0b6\uc744 \uc601\uc704\ud560 \uc218 \uc788\uc2b5\ub2c8\ub2e4.\u00a4<sup>7<\/sup><\/p>\n\n <p>\ud310\ucf54\ub2c8 \uc99d\ud6c4\uad70\uc758 \uc8fc\uc694 \ud2b9\uc9d5\uc740 \uac70\uc758 \ubaa8\ub4e0 \uc544\ubbf8\ub178\uc0b0\uc774 \uc18c\ubcc0\uc5d0\uc11c \uacfc\uc789\uc73c\ub85c \ubc1c\uacac\ub418\ub294 \uc804\uc2e0\uc131 \uc544\ubbf8\ub178\uc0b0\ub1e8\uc99d\uc785\ub2c8\ub2e4.\u00a4<sup>6<\/sup> \uadf8\ub7ec\ub098 \uc2dd\uc774 \uc12d\ucde8\uc640 \uad00\ub828\ud558\uc5ec \uc190\uc2e4\uc774 \ubbf8\ubbf8\ud558\uae30 \ub54c\ubb38\uc5d0 \uc77c\ubc18\uc801\uc73c\ub85c \uc99d\ud6c4\uad70\uc758 \uc774\ub7ec\ud55c \ud2b9\uc815 \uce21\uba74\uc73c\ub85c \uc778\ud55c \uc784\uc0c1\uc801 \uacb0\uacfc\ub294 \uc5c6\uc2b5\ub2c8\ub2e4.\u00a4<sup>6<\/sup><\/p>\n\n <p>\uc601\uc544\uc758 \uc544\ubbf8\ub178\uc0b0 \uc218\uce58\uac00 \uc99d\uac00\ud588\ub294\uc9c0 \uac80\uc0ac\ud558\ub294 \uac83\uc740 \uc2e0\uc9c4\ub300\uc0ac \ubb38\uc81c\ub97c \uc870\uae30\uc5d0 \ubc1c\uacac\ud558\ub294 \ub370 \ub3c4\uc6c0\uc774 \ub420 \uc218 \uc788\uc2b5\ub2c8\ub2e4. \uc774\ub7ec\ud55c \uc9c8\ud658\uc744 \uc870\uae30\uc5d0 \uce58\ub8cc\ud558\uba74 \ud5a5\ud6c4 \ud569\ubcd1\uc99d\uc744 \uc608\ubc29\ud560 \uc218 \uc788\uc2b5\ub2c8\ub2e4.<sup>2<\/sup><\/p> <p>\uc2dc\uc2a4\ud2f4\ub1e8\uc99d\uc740 \uc0c1\uc5fc\uc0c9\uccb4 \uc5f4\uc131 \uc720\uc804\uc9c8\ud658\uc73c\ub85c \uc804\uccb4 \uc694\ub85c\uacb0\uc11d\uc758 1-2%\ub97c \ucc28\uc9c0\ud569\ub2c8\ub2e4. \uc18c\uc544 \uc694\ub85c\uacb0\uc11d \ud658\uc790\uc5d0\uc11c\ub294 \ucd5c\ub300 8%\uae4c\uc9c0 \ubcf4\uace0\ub429\ub2c8\ub2e4. EAU \uacb0\uc11d \uac00\uc774\ub4dc\ub77c\uc778\uc5d0 \ub530\ub974\uba74, \uce58\ub8cc\ub294 \uacfc\ub2e4 \uc218\ubd84 \uc12d\ucde8(\uc77c\uc77c \uc18c\ubcc0\ub7c9 3L \uc774\uc0c1 \uc720\uc9c0), \uc18c\ubcc0 \uc54c\uce7c\ub9ac\ud654(pH 7.0-7.5), \ud544\uc694\uc2dc \ud2f0\uc624\ud504\ub85c\ub2cc(tiopronin) \ud22c\uc5ec\ub97c \ud3ec\ud568\ud569\ub2c8\ub2e4.<\/p>","gt-related-evidence":null,"gt-featured":true,"gt-ai-referenced":false,"gt-view-count":66},"yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v27.7 (Yoast SEO v27.7) - https:\/\/yoast.com\/product\/yoast-seo-premium-wordpress\/ -->\n<title>\uc544\ubbf8\ub178\uc0b0\ub1e8 | \uc2e0\uc138\uad00 \uae30\ub2a5 \uc7a5\uc560\uc640 \uc694\ub85c\uacb0\uc11d \uc704\ud5d8<\/title>\n<meta name=\"description\" content=\"\uc544\ubbf8\ub178\uc0b0\ub1e8\ub294 \uc18c\ubcc0\uc5d0\uc11c \ube44\uc815\uc0c1\uc801\uc73c\ub85c \ub9ce\uc740 \uc544\ubbf8\ub178\uc0b0\uc774 \ubc30\uc124\ub418\ub294 \uc2e0\uc138\uad00 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