{"id":11996,"date":"2025-07-22T08:25:54","date_gmt":"2025-07-22T12:25:54","guid":{"rendered":"https:\/\/www.rigicon.com\/glossary-term\/angiomyolipoma\/"},"modified":"2025-07-22T08:25:54","modified_gmt":"2025-07-22T12:25:54","slug":"angiomiolipoma","status":"publish","type":"glossary-term","link":"https:\/\/www.rigicon.com\/es\/glossary-term\/angiomiolipoma\/","title":{"rendered":"Angiomiolipoma"},"content":{"rendered":"","protected":false},"excerpt":{"rendered":"","protected":false},"featured_media":0,"template":"","glossary-category":[126],"glossary-product":[],"class_list":["post-11996","glossary-term","type-glossary-term","status-publish","hentry","glossary-category-urological-conditions"],"acf":{"gt-definition":"<p>\n        El angiomiolipoma es un tumor renal benigno caracterizado por una composici\u00f3n de vasos sangu\u00edneos, m\u00fasculo liso y tejido adiposo en cantidades variables.<span class=\"citation\">1<\/span> Pertenece a la familia de tumores de c\u00e9lulas epitelioides perivasculares (PEComas) y se distingue por su diferenciaci\u00f3n epitelioide perivascular.<span class=\"citation\">2<\/span> Estos tumores suelen estar bien circunscritos y pueden variar en tama\u00f1o desde unos pocos mil\u00edmetros. hasta m\u00e1s de 20 cent\u00edmetros de di\u00e1metro.<span class=\"citation\">3<\/span> Aunque se consideran benignos, los angiomiolipomas pueden crecer significativamente y pueden causar complicaciones por efecto de masa o hemorragia espont\u00e1nea debido a la presencia de vasos sangu\u00edneos anormales con microaneurismas.<span class=\"citation\">4<\/span> Los angiomiolipomas pueden manifestarse como masas ricas en grasa (m\u00e1s com\u00fan), pobres en grasa o invisibles en grasa, y aproximadamente el 5% pertenece al Variedad pobre en grasa o invisible en grasa, que presenta desaf\u00edos de diagn\u00f3stico.<span class=\"citation\">5<\/span>\n    <\/p>","gt-synonyms":"Angiomiolipoma renal (AML), Angiomiolipoma renal, LMA renal, LMA renal, Hamartoma renal (aunque t\u00e9cnicamente distinto)","gt-citation":"[1] Skelton WP, Dahlen T, Patel H, et al. Renal Angiomyolipoma. StatPearls. 2024. https:\/\/www.ncbi.nlm.nih.gov\/books\/NBK585104\/\n\n[2] Jinzaki M, Silverman SG, Akita H, et al. Renal angiomyolipoma: a radiological classification and update on recent developments in diagnosis and management. Abdom Imaging. 2014;39(3):588-604. DOI: 10.1007\/s00261-014-0083-3\n\n[3] Flum AS, Hamoui N, Said MA, et al. Update on the Diagnosis and Management of Renal Angiomyolipoma. J Urol. 2016;195(4 Pt 1):834-846. DOI: 10.1016\/j.juro.2015.07.126\n\n[4] Bissler JJ, Kingswood JC. Renal angiomyolipomata. Kidney Int. 2018;93(6):1282-1294. DOI: 10.1016\/j.kint.2017.12.020\n\n[5] Vos N, Oyen R. Renal Angiomyolipoma: The Good, the Bad, and the Ugly. J Belg Soc Radiol. 2018;102(1):41. DOI: 10.5334\/jbsr.1536","gt-clinical-context":"<p>\n        Los angiomiolipomas son cl\u00ednicamente significativos tanto en contextos espor\u00e1dicos como hereditarios. La mayor\u00eda (80%) ocurren espor\u00e1dicamente, mientras que el 20% est\u00e1n asociados con condiciones gen\u00e9ticas, principalmente complejo de esclerosis tuberosa (TSC) y linfangioleiomiomatosis pulmonar (LAM).<span class=\"citation\">1<\/span>\n    <\/p>\n    <p>\n        En la pr\u00e1ctica cl\u00ednica, los angiomiolipomas a menudo se descubren incidentalmente durante estudios de imagen realizados por razones no relacionadas.<span class=\"citation\">2<\/span> Sin embargo, las presentaciones sintom\u00e1ticas pueden incluir dolor en el flanco, masa palpable, infecciones del tracto urinario, hematuria, insuficiencia renal o hipertensi\u00f3n.<span class=\"citation\">3<\/span> La presentaci\u00f3n cl\u00ednica m\u00e1s preocupante es la hemorragia retroperitoneal espont\u00e1nea, que puede poner en peligro la vida y es m\u00e1s com\u00fan en tumores m\u00e1s grandes que 4 cm de di\u00e1metro.<span class=\"citation\">4<\/span>\n    <\/p>\n    <p>\n        La selecci\u00f3n de pacientes para la intervenci\u00f3n se basa en varios factores que incluyen el tama\u00f1o del tumor, los s\u00edntomas, el riesgo de complicaciones y las condiciones asociadas. Para angiomiolipomas peque\u00f1os (<4 cm) asintom\u00e1ticos, generalmente se recomienda vigilancia activa con im\u00e1genes peri\u00f3dicas.<span class=\"citation\">2<\/span> Para tumores m\u00e1s grandes, lesiones sintom\u00e1ticas o aquellos con alto riesgo de sangrado, se puede justificar la intervenci\u00f3n.<span class=\"citation\">5<\/span>\n    <\/p>\n    <p>\n        Las opciones de tratamiento incluyen:\n    <\/p>\n    <ul>\n        <li>Vigilancia activa con im\u00e1genes peri\u00f3dicas para tumores peque\u00f1os y asintom\u00e1ticos<\/li>\n        <li>Embolizaci\u00f3n arterial selectiva para controlar el sangrado o reducir el tama\u00f1o del tumor<\/li>\n        <li>Cirug\u00eda conservadora de nefronas (nefrectom\u00eda parcial) para casos seleccionados<\/li>\n        <li>Terapia farmacol\u00f3gica con inhibidores de la diana de rapamicina (mTOR) en mam\u00edferos, como sirolimus o everolimus, particularmente para pacientes con complejo de esclerosis tuberosa<span class=\"citation\">4<\/span><\/li>\n    <\/ul>\n    <p>\n        Para los pacientes con complejo de esclerosis tuberosa, se recomienda la detecci\u00f3n de angiomiolipomas renales, ya que estos pacientes a menudo desarrollan m\u00faltiples tumores bilaterales que pueden requerir una intervenci\u00f3n temprana.<span class=\"citation\">1<\/span> De manera similar, los pacientes con linfangioleiomiomatosis deben someterse a im\u00e1genes renales para detectar angiomiolipomas.<span class=\"citation\">5<\/span>\n    <\/p>","gt-related-evidence":null,"gt-featured":true,"gt-ai-referenced":false,"gt-view-count":56},"yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v28.0 (Yoast SEO v28.0) - https:\/\/yoast.com\/product\/yoast-seo-premium-wordpress\/ -->\n<title>Angiomiolipoma: Benign Kidney Tumor Composed of Blood...<\/title>\n<meta name=\"description\" content=\"El angiomiolipoma es un tumor renal benigno formado por vasos sangu\u00edneos, m\u00fasculo liso y tejido 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